Multiple familial trichoepithelioma: confirmation via dermoscopy

نویسندگان

  • Cristián Navarrete-Dechent
  • Shirin Bajaj
  • Ashfaq A. Marghoob
  • Sergio González
  • Daniel Muñoz
چکیده

Trichoepitheliomas are uncommon benign adnexal neoplasms that originate from the hair follicles. Multiple familial trichoepithelioma constitute an autosomal dominant disease characterized by the appearance of multiple flesh-colored, symmetrical papules, tumors and/or nodules in the central face and occasionally on the scalp. Although clinical diagnosis is usually straightforward in light of the family history and naked-eye examination, dermoscopy may aid in its confirmation. Dermoscopy of each papule revealed in-focus arborizing vessels, multiple milia-like cysts and rosettes amidst a whitish background. In a patient with multiple facial papules revealing a dermoscopic appearance described above, the diagnosis of sporadic or familial multiple trichoepithelioma should be considered.

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عنوان ژورنال:

دوره 6  شماره 

صفحات  -

تاریخ انتشار 2016